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Adherence and Barriers to Hyperinsufflation in Children with Congenital Muscular Dystrophy

BACKGROUND: Congenital muscular dystrophy (CMD) is a rare, inherited neuromuscular disease characterized by progressive muscle weakness, thoracic insufficiency and ultimately respiratory failure. Adherence to respiratory therapies in children with neuromuscular disorders is unknown. This study exami...

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Detalhes bibliográficos
Publicado no:Pediatr Pulmonol
Main Authors: Pascoe, John E., Sawnani, Hemant, Mayer, Oscar H., McConnell, Keith, McDonough, Joseph M., White, Cynthia, Rutkowski, Anne M., Amin, Raouf S., Modi, Avani C.
Formato: Artigo
Idioma:Inglês
Publicado em: 2016
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6827716/
https://ncbi.nlm.nih.gov/pubmed/27875025
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ppul.23645
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