Caricamento...

Large neutral amino acid status in association with P:T ratio and diet in adult and pediatric patients with phenylketonuria

BACKGROUND: Intake of large neutral amino acids (LNAA) may inhibit phenylalanine (PHE) transport across the blood brain barrier and assist with blood PHE control in patients with phenylketonuria (PKU). We evaluated the interrelationship between LNAA in plasma and diet on Phe:Tyr (P:T) ratio in patie...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Pubblicato in:JIMD Rep
Autori principali: Douglas, Teresa D., Nucci, Anita M., Berry, Ann M., Henes, Sarah T., Singh, Rani H.
Natura: Artigo
Lingua:Inglês
Pubblicazione: John Wiley & Sons, Inc. 2019
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6850973/
https://ncbi.nlm.nih.gov/pubmed/31741827
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jmd2.12076
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !