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Pneumothorax as a Presentation of Tuberous Sclerosis-Associated Lymphangioleiomyomatosis

Tuberous sclerosis complex (TSC) is a rare, autosomal dominant disorder with a recognized phenotypic variability with clinical manifestations developing continuously throughout life. The follow-up of TSC patients is challenging. The authors present a case with a definite diagnosis of TSC with known...

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Publicado en:Eur J Case Rep Intern Med
Autores principales: Silva, Duarte Lages, Pinto, Pedro, Costa, Miguel, Maia, Rosana, Rodrigues, Carmélia
Formato: Artigo
Lenguaje:Inglês
Publicado: SMC Media Srl 2019
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6822674/
https://ncbi.nlm.nih.gov/pubmed/31742202
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.12890/2019_001264
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