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Tuberous sclerosis complex presenting as pulmonary lymphangioleiomyomatosis - a clinicoradiological diagnosis

Tuberous sclerosis complex (TSC) manifests predominantly as a neurocutaneous disorder. Lymphangioleiomyomatosis (LAM) is a rare pulmonary manifestation of TSC. Imaging evaluation plays an important role in the assessment of patients with tuberous sclerosis complex. In newly diagnosed patients, it he...

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Detaylı Bibliyografya
Yayımlandı:Pan Afr Med J
Asıl Yazarlar: Gupta, Kamini, Goyal, Amit, Saggar, Kavita, Banerjee, Avik
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: The African Field Epidemiology Network 2015
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC4470415/
https://ncbi.nlm.nih.gov/pubmed/26113938
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.11604/pamj.2015.20.207.5490
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