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Tuberous sclerosis complex presenting as pulmonary lymphangioleiomyomatosis - a clinicoradiological diagnosis

Tuberous sclerosis complex (TSC) manifests predominantly as a neurocutaneous disorder. Lymphangioleiomyomatosis (LAM) is a rare pulmonary manifestation of TSC. Imaging evaluation plays an important role in the assessment of patients with tuberous sclerosis complex. In newly diagnosed patients, it he...

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Bibliografske podrobnosti
izdano v:Pan Afr Med J
Main Authors: Gupta, Kamini, Goyal, Amit, Saggar, Kavita, Banerjee, Avik
Format: Artigo
Jezik:Inglês
Izdano: The African Field Epidemiology Network 2015
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC4470415/
https://ncbi.nlm.nih.gov/pubmed/26113938
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.11604/pamj.2015.20.207.5490
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