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Fibulin-1c regulates transforming growth factor–β activation in pulmonary tissue fibrosis

Tissue remodeling/fibrosis is a major feature of all fibrotic diseases, including idiopathic pulmonary fibrosis (IPF). It is underpinned by accumulating extracellular matrix (ECM) proteins. Fibulin-1c (Fbln1c) is a matricellular ECM protein associated with lung fibrosis in both humans and mice and s...

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Bibliografiset tiedot
Julkaisussa:JCI Insight
Päätekijät: Liu, Gang, Cooley, Marion A., Jarnicki, Andrew G., Borghuis, Theo, Nair, Prema M., Tjin, Gavin, Hsu, Alan C., Haw, Tatt Jhong, Fricker, Michael, Harrison, Celeste L., Jones, Bernadette, Hansbro, Nicole G., Wark, Peter A., Horvat, Jay C., Argraves, W. Scott, Oliver, Brian G., Knight, Darryl A., Burgess, Janette K., Hansbro, Philip M.
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: American Society for Clinical Investigation 2019
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC6777837/
https://ncbi.nlm.nih.gov/pubmed/31343988
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/jci.insight.124529
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