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Fibulins: physiological and disease perspectives

The fibulins are a family of proteins that are associated with basement membranes and elastic extracellular matrix fibres. This review summarizes findings from studies of animal models of fibulin deficiency, human fibulin gene mutations, human tumours and injury models that have advanced our underst...

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Autori principali: Argraves, W. Scott, Greene, Lisa M., Cooley, Marion A., Gallagher, William M.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2003
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC1326425/
https://ncbi.nlm.nih.gov/pubmed/14647206
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/sj.embor.7400033
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