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Desmosterolosis and desmosterol homeostasis in the developing mouse brain
Cholesterol serves as a building material for cellular membranes and plays an important role in cellular metabolism. The brain relies on its own cholesterol biosynthesis, which starts during embryonic development. Cholesterol is synthesized from two immediate precursors, desmosterol and 7-DHC. Mutat...
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| Опубликовано в: : | J Inherit Metab Dis |
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| Главные авторы: | , , , , |
| Формат: | Artigo |
| Язык: | Inglês |
| Опубликовано: |
2019
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| Предметы: | |
| Online-ссылка: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6739189/ https://ncbi.nlm.nih.gov/pubmed/30891795 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jimd.12088 |
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