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Expert Consensus Recommendations for the Suspicion and Diagnosis of Cardiac ATTR Amyloidosis

Cardiomyopathy is a manifestation of transthyretin amyloid (ATTR) amyloidosis, which is an underrecognized systemic disease whereby the transthyretin protein misfolds to form fibrils that deposit in various tissues and organs. ATTR amyloidosis is debilitating and associated with poor life expectancy...

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Pubblicato in:Circ Heart Fail
Autori principali: Maurer, Mathew S., Bokhari, Sabahat, Damy, Thibaud, Dorbala, Sharmila, Drachman, Brian M., Fontana, Marianna, Grogan, Martha, Kristen, Arnt V., Lousada, Isabelle, Nativi-Nicolau, Jose, Quarta, Candida Cristina, Rapezzi, Claudio, Ruberg, Frederick L., Witteles, Ronald, Merlini, Giampaolo
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2019
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6736650/
https://ncbi.nlm.nih.gov/pubmed/31480867
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1161/CIRCHEARTFAILURE.119.006075
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