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Expert Consensus Recommendations for the Suspicion and Diagnosis of Cardiac ATTR Amyloidosis

Cardiomyopathy is a manifestation of transthyretin amyloid (ATTR) amyloidosis, which is an underrecognized systemic disease whereby the transthyretin protein misfolds to form fibrils that deposit in various tissues and organs. ATTR amyloidosis is debilitating and associated with poor life expectancy...

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Vydáno v:Circ Heart Fail
Hlavní autoři: Maurer, Mathew S., Bokhari, Sabahat, Damy, Thibaud, Dorbala, Sharmila, Drachman, Brian M., Fontana, Marianna, Grogan, Martha, Kristen, Arnt V., Lousada, Isabelle, Nativi-Nicolau, Jose, Quarta, Candida Cristina, Rapezzi, Claudio, Ruberg, Frederick L., Witteles, Ronald, Merlini, Giampaolo
Médium: Artigo
Jazyk:Inglês
Vydáno: 2019
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC6736650/
https://ncbi.nlm.nih.gov/pubmed/31480867
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1161/CIRCHEARTFAILURE.119.006075
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