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Glycoproteomic Analysis of the Aortic Extracellular Matrix in Marfan Patients

Marfan syndrome (MFS) is caused by mutations in FBN1 (fibrillin-1), an extracellular matrix (ECM) component, which is modified post-translationally by glycosylation. This study aimed to characterize the glycoproteome of the aortic ECM from patients with MFS and relate it to aortopathy. APPROACH AND...

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Опубликовано в: :Arterioscler Thromb Vasc Biol
Главные авторы: Yin (殷晓科), Xiaoke, Wanga, Shaynah, Fellows, Adam L., Barallobre-Barreiro, Javier, Lu, Ruifang, Davaapil, Hongorzul, Franken, Romy, Fava, Marika, Baig, Ferheen, Skroblin, Philipp, Xing, Qiuru, Koolbergen, David R., Groenink, Maarten, Zwinderman, Aeilko H., Balm, Ron, de Vries, Carlie J.M., Mulder, Barbara J.M., Viner, Rosa, Jahangiri, Marjan, Reinhardt, Dieter P., Sinha, Sanjay, de Waard, Vivian, Mayr, Manuel
Формат: Artigo
Язык:Inglês
Опубликовано: Lippincott Williams & Wilkins 2019
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Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC6727943/
https://ncbi.nlm.nih.gov/pubmed/31315432
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1161/ATVBAHA.118.312175
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