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Severe neonatal multiple sulfatase deficiency presenting with hydrops fetalis in a preterm birth patient

Multiple sulfatase deficiency (MSD) is an ultra‐rare lysosomal storage disorder (LSD). Mutations in the SUMF1 gene encoding the formylglycine generating enzyme (FGE) result in an unstable FGE protein with reduced enzymatic activity, thereby affecting the posttranslational activation of newly synthes...

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Dettagli Bibliografici
Pubblicato in:JIMD Rep
Autori principali: Schlotawa, Lars, Dierks, Thomas, Christoph, Sophie, Cloppenburg, Eva, Ohlenbusch, Andreas, Korenke, G. Christoph, Gärtner, Jutta
Natura: Artigo
Lingua:Inglês
Pubblicazione: John Wiley & Sons, Inc. 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6718111/
https://ncbi.nlm.nih.gov/pubmed/31497481
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jmd2.12074
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