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Pathobiology of inherited biliary diseases: a roadmap to understand acquired liver diseases

Bile duct epithelial cells, also known as cholangiocytes, regulate the composition of bile and its flow. Acquired, congenital and genetic dysfunctions in these cells give rise to a set of diverse and complex diseases, often of unknown aetiology, called cholangiopathies. New knowledge has been steadi...

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Dettagli Bibliografici
Pubblicato in:Nat Rev Gastroenterol Hepatol
Autori principali: Fabris, Luca, Fiorotto, Romina, Spirli, Carlo, Cadamuro, Massimiliano, Mariotti, Valeria, Perugorria, Maria J., Banales, Jesus M., Strazzabosco, Mario
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6661007/
https://ncbi.nlm.nih.gov/pubmed/31165788
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41575-019-0156-4
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