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Diastolic subclinical primary alterations in marfan syndrome and marfan‐related disorders

Background: The extracellular matrix tissue of the myocardium importantly contributes to left ventricular (LV) performance. Inherited connective tissue disorders related to the FBN1 gene could involve cardiac interstitium resulting in functional abnormalities. Hypothesis: To disclose a primary invol...

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Detalles Bibliográficos
Publicado en:Clin Cardiol
Main Authors: Porciani, Maria Cristina, Giurlani, Letizia, Chelucci, Andrea, Pepe, Guglielmina, Giusti, Betti, Brunelli, Tamara, Attanasio, Monica, Martinucci, Pietro, Fattori, Rossella, Abbatea, Rosanna, Gensini, Gian Franco
Formato: Artigo
Idioma:Inglês
Publicado: Wiley Periodicals, Inc. 2006
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6654107/
https://ncbi.nlm.nih.gov/pubmed/12269520
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/clc.4960250905
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