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Diastolic subclinical primary alterations in marfan syndrome and marfan‐related disorders

Background: The extracellular matrix tissue of the myocardium importantly contributes to left ventricular (LV) performance. Inherited connective tissue disorders related to the FBN1 gene could involve cardiac interstitium resulting in functional abnormalities. Hypothesis: To disclose a primary invol...

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Bibliografske podrobnosti
izdano v:Clin Cardiol
Main Authors: Porciani, Maria Cristina, Giurlani, Letizia, Chelucci, Andrea, Pepe, Guglielmina, Giusti, Betti, Brunelli, Tamara, Attanasio, Monica, Martinucci, Pietro, Fattori, Rossella, Abbatea, Rosanna, Gensini, Gian Franco
Format: Artigo
Jezik:Inglês
Izdano: Wiley Periodicals, Inc. 2006
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC6654107/
https://ncbi.nlm.nih.gov/pubmed/12269520
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/clc.4960250905
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