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Diastolic subclinical primary alterations in marfan syndrome and marfan‐related disorders

Background: The extracellular matrix tissue of the myocardium importantly contributes to left ventricular (LV) performance. Inherited connective tissue disorders related to the FBN1 gene could involve cardiac interstitium resulting in functional abnormalities. Hypothesis: To disclose a primary invol...

詳細記述

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書誌詳細
出版年:Clin Cardiol
主要な著者: Porciani, Maria Cristina, Giurlani, Letizia, Chelucci, Andrea, Pepe, Guglielmina, Giusti, Betti, Brunelli, Tamara, Attanasio, Monica, Martinucci, Pietro, Fattori, Rossella, Abbatea, Rosanna, Gensini, Gian Franco
フォーマット: Artigo
言語:Inglês
出版事項: Wiley Periodicals, Inc. 2006
主題:
オンライン・アクセス:https://ncbi.nlm.nih.gov/pmc/articles/PMC6654107/
https://ncbi.nlm.nih.gov/pubmed/12269520
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/clc.4960250905
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