Chargement en cours...

Marfan syndrome: current perspectives

Marfan syndrome (MFS) is a pleiotropic connective tissue disease inherited as an autosomal dominant trait, due to mutations in the FBN1 gene encoding fibrillin 1. It is an important protein of the extracellular matrix that contributes to the final structure of a microfibril. Few cases displaying an...

Description complète

Enregistré dans:
Détails bibliographiques
Publié dans:Appl Clin Genet
Auteurs principaux: Pepe, Guglielmina, Giusti, Betti, Sticchi, Elena, Abbate, Rosanna, Gensini, Gian Franco, Nistri, Stefano
Format: Artigo
Langue:Inglês
Publié: Dove Medical Press 2016
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4869846/
https://ncbi.nlm.nih.gov/pubmed/27274304
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2147/TACG.S96233
Tags: Ajouter un tag
Pas de tags, Soyez le premier à ajouter un tag!