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Sex Differences in Vascular Reactivity in Mesenteric Arteries from a Mouse Model of Acute Intermittent Porphyria

BACKGROUND AND AIMS: Acute intermittent porphyria (AIP) results from a partial deficiency of porphobilinogen deaminase (PBGD). Symptomatic AIP patients, most of whom are women, experience acute attacks characterized by severe abdominal pain and abrupt increases in blood pressure. Here, we characteri...

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Publicado en:Mol Genet Metab
Main Authors: Pulgar, Victor M., Yasuda, Makiko, Gan, Lin, Desnick, Robert J., Bonkovsky, Herbert L.
Formato: Artigo
Idioma:Inglês
Publicado: 2019
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6612470/
https://ncbi.nlm.nih.gov/pubmed/30639047
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ymgme.2019.01.005
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