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Mechanisms of thrombocytopenia in platelet-type von Willebrand disease

Platelet-type von Willebrand disease is an inherited platelet disorder characterized by thrombocytopenia with large platelets caused by gain-of-function variants in GP1BA leading to enhanced GPIbα-von Willebrand factor (vWF) interaction. GPIbα and vWF play a role in megakaryocytopoiesis, thus we aim...

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Dades bibliogràfiques
Publicat a:Haematologica
Autors principals: Bury, Loredana, Malara, Alessandro, Momi, Stefania, Petito, Eleonora, Balduini, Alessandra, Gresele, Paolo
Format: Artigo
Idioma:Inglês
Publicat: Ferrata Storti Foundation 2019
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6601082/
https://ncbi.nlm.nih.gov/pubmed/30655369
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3324/haematol.2018.200378
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