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Modified Atkins ketogenic diet improves heart and skeletal muscle function in glycogen storage disease type III

Glycogen storage disease type III (GSDIII) management in adult patients includes a high-protein diet with cornstarch supplementation to maintain a normal level of glucose in the blood. This regimen can prevent hypoglycaemia but does not seem to improve skeletal muscle and heart function. A 34 years-...

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Shranjeno v:
Bibliografske podrobnosti
izdano v:Acta Myol
Main Authors: FRANCINI-PESENTI, FRANCESCO, TRESSO, SILVIA, VITTURI, NICOLA
Format: Artigo
Jezik:Inglês
Izdano: Pacini Editore srl 2019
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC6598403/
https://ncbi.nlm.nih.gov/pubmed/31309177
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