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Neoplasm Risk Among Individuals With a Pathogenic Germline Variant in DICER1

PURPOSE: DICER1 syndrome is an autosomal-dominant, pleiotropic tumor-predisposition disorder caused by pathogenic germline variants in DICER1. We sought to quantify risk, hazard rates, and the probability of neoplasm incidence accounting for competing risks (“cumulative incidence”) of neoplasms (ben...

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Detalhes bibliográficos
Publicado no:J Clin Oncol
Main Authors: Stewart, Douglas R., Best, Ana F., Williams, Gretchen M., Harney, Laura A., Carr, Ann G., Harris, Anne K., Kratz, Christian P., Dehner, Louis P., Messinger, Yoav H., Rosenberg, Philip S., Hill, D. Ashley, Schultz, Kris Ann P.
Formato: Artigo
Idioma:Inglês
Publicado em: American Society of Clinical Oncology 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6553836/
https://ncbi.nlm.nih.gov/pubmed/30715996
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1200/JCO.2018.78.4678
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