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Successful treatment of noncirrhotic portal hypertension with eculizumab in paroxysmal nocturnal hemoglobinuria: A case report

BACKGROUND: Idiopathic non-cirrhotic portal hypertension (INCPH) is mainly associated with thrombophilia in Western countries. Paroxysmal nocturnal hemoglobinuria (PNH) is a rare hematologic disease that manifests with hemolytic anemia, thrombosis, and peripheral blood cytopenias. Portal and hepatic...

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Publicado en:World J Hepatol
Main Authors: Alexopoulou, Alexandra, Mani, Iliana, Tiniakos, Dina G, Kontopidou, Flora, Tsironi, Ioanna, Noutsou, Marina, Pantelidaki, Helen, Dourakis, Spyros P
Formato: Artigo
Idioma:Inglês
Publicado: Baishideng Publishing Group Inc 2019
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6547289/
https://ncbi.nlm.nih.gov/pubmed/31183008
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4254/wjh.v11.i5.483
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