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A randomised controlled trial evaluating arrhythmia burden, risk of sudden cardiac death and stroke in patients with Fabry disease: the role of implantable loop recorders (RaILRoAD) compared with current standard practice

BACKGROUND: Fabry disease (FD) is a genetic disorder caused by a deficiency in the enzyme alpha-galactosidase A, leading to an accumulation of glycosphingolipids in tissues across the body. Cardiac disease is the leading cause of morbidity and mortality. Advanced disease, characterised by extensive...

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Publicado en:Trials
Autores principales: Vijapurapu, Ravi, Kozor, Rebecca, Hughes, Derralynn A., Woolfson, Peter, Jovanovic, Ana, Deegan, Patrick, Rusk, Rosemary, Figtree, Gemma A., Tchan, Michel, Whalley, David, Kotecha, Dipak, Leyva, Francisco, Moon, James, Geberhiwot, Tarekegn, Steeds, Richard P.
Formato: Artigo
Lenguaje:Inglês
Publicado: BioMed Central 2019
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6544923/
https://ncbi.nlm.nih.gov/pubmed/31151481
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13063-019-3425-1
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