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Spirometric indices in primary ciliary dyskinesia: systematic review and meta-analysis

Primary ciliary dyskinesia (PCD) is a genetic, heterogeneous disease caused by dysfunction of cilia. Evidence is sparse and reports of lung function in PCD patients range from normal to severe impairment. This systematic review and meta-analysis of studies of lung function in PCD patients examines t...

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Dades bibliogràfiques
Publicat a:ERJ Open Res
Autors principals: Halbeisen, Florian S., Jose, Anu, de Jong, Carmen, Nyilas, Sylvia, Latzin, Philipp, Kuehni, Claudia E., Goutaki, Myrofora
Format: Artigo
Idioma:Inglês
Publicat: European Respiratory Society 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6513038/
https://ncbi.nlm.nih.gov/pubmed/31111042
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1183/23120541.00231-2018
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