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EGFP Tags Affect Cellular Localization of ATP7B Mutants

AIMS: Wilson's disease is an autosomal recessive disorder of copper metabolism due to mutations within ATP7B gene. Clinical investigations indicate that ATP7B truncations are associated with an early age of onset when compared to its missense mutations. In vitro studies show that mislocalizatio...

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Publicat a:CNS Neurosci Ther
Autors principals: Zhu, Min, Ni, Wang, Dong, Yi, Wu, Zhi‐Ying
Format: Artigo
Idioma:Inglês
Publicat: John Wiley and Sons Inc. 2013
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6493502/
https://ncbi.nlm.nih.gov/pubmed/23607698
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/cns.12091
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