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A post-translational modification code for CFTR maturation is altered in cystic fibrosis

The multistep process regulating the maturation of membrane proteins in the endoplasmic reticulum (ER) and the secretory pathway is disrupted in many protein misfolding disorders. Mutations in the ion channel CFTR that impair its folding and subsequent localization to the plasma membrane cause cysti...

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Detalhes bibliográficos
Publicado no:Sci Signal
Main Authors: Pankow, Sandra, Bamberger, Casimir, Yates, John R.
Formato: Artigo
Idioma:Inglês
Publicado em: 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6464640/
https://ncbi.nlm.nih.gov/pubmed/30600261
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1126/scisignal.aan7984
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