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The ADAMTS13–VWF axis is dysregulated in chronic thromboembolic pulmonary hypertension

Chronic thromboembolic pulmonary hypertension (CTEPH) is an important consequence of pulmonary embolism that is associated with abnormalities in haemostasis. We investigated the ADAMTS13–von Willebrand factor (VWF) axis in CTEPH, including its relationship with disease severity, inflammation, ABO gr...

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Bibliografski detalji
Izdano u:Eur Respir J
Glavni autori: Newnham, Michael, South, Kieron, Bleda, Marta, Auger, William R., Barberà, Joan A., Bogaard, Harm, Bunclark, Katherine, Cannon, John E., Delcroix, Marion, Hadinnapola, Charaka, Howard, Luke S., Jenkins, David, Mayer, Eckhard, Ng, Choo, Rhodes, Christopher J., Screaton, Nicholas, Sheares, Karen, Simpson, Michael A., Southwood, Mark, Su, Li, Taboada, Dolores, Traylor, Matthew, Trembath, Richard C., Villar, Sofia S., Wilkins, Martin R., Wharton, John, Gräf, Stefan, Pepke-Zaba, Joanna, Laffan, Michael, Lane, David A., Morrell, Nicholas W., Toshner, Mark
Format: Artigo
Jezik:Inglês
Izdano: European Respiratory Society 2019
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC6437602/
https://ncbi.nlm.nih.gov/pubmed/30655285
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1183/13993003.01805-2018
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