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The ADAMTS13–VWF axis is dysregulated in chronic thromboembolic pulmonary hypertension

Chronic thromboembolic pulmonary hypertension (CTEPH) is an important consequence of pulmonary embolism that is associated with abnormalities in haemostasis. We investigated the ADAMTS13–von Willebrand factor (VWF) axis in CTEPH, including its relationship with disease severity, inflammation, ABO gr...

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Detalhes bibliográficos
Publicado no:Eur Respir J
Main Authors: Newnham, Michael, South, Kieron, Bleda, Marta, Auger, William R., Barberà, Joan A., Bogaard, Harm, Bunclark, Katherine, Cannon, John E., Delcroix, Marion, Hadinnapola, Charaka, Howard, Luke S., Jenkins, David, Mayer, Eckhard, Ng, Choo, Rhodes, Christopher J., Screaton, Nicholas, Sheares, Karen, Simpson, Michael A., Southwood, Mark, Su, Li, Taboada, Dolores, Traylor, Matthew, Trembath, Richard C., Villar, Sofia S., Wilkins, Martin R., Wharton, John, Gräf, Stefan, Pepke-Zaba, Joanna, Laffan, Michael, Lane, David A., Morrell, Nicholas W., Toshner, Mark
Formato: Artigo
Idioma:Inglês
Publicado em: European Respiratory Society 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6437602/
https://ncbi.nlm.nih.gov/pubmed/30655285
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1183/13993003.01805-2018
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