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Restoring mitofusin balance prevents axonal degeneration in a Charcot-Marie-Tooth type 2A model

Mitofusin-2 (MFN2) is a mitochondrial outer-membrane protein that plays a pivotal role in mitochondrial dynamics in most tissues, yet mutations in MFN2, which cause Charcot-Marie-Tooth disease type 2A (CMT2A), primarily affect the nervous system. We generated a transgenic mouse model of CMT2A that d...

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Dettagli Bibliografici
Pubblicato in:J Clin Invest
Autori principali: Zhou, Yueqin, Carmona, Sharon, Muhammad, A.K.M.G., Bell, Shaughn, Landeros, Jesse, Vazquez, Michael, Ho, Ritchie, Franco, Antonietta, Lu, Bin, Dorn, Gerald W., Wang, Shaomei, Lutz, Cathleen M., Baloh, Robert H.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Clinical Investigation 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6436852/
https://ncbi.nlm.nih.gov/pubmed/30882371
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/JCI124194
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