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Genomic correction of familial cardiomyopathy in human engineered cardiac tissues

In this study, we used three-dimensional human engineered cardiac tissue technology to directly show that phospholamban (PLN) R14del mutation impairs cardiac contractility and to demonstrate restoration of contractile properties with targeted genetic correction of this inheritable form of dilated ca...

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Podrobná bibliografie
Vydáno v:Eur Heart J
Hlavní autoři: Stillitano, Francesca, Turnbull, Irene C., Karakikes, Ioannis, Nonnenmacher, Mathieu, Backeris, Peter, Hulot, Jean-Sébastien, Kranias, Evangelia G., Hajjar, Roger J., Costa, Kevin D.
Médium: Artigo
Jazyk:Inglês
Vydáno: European Society of Cardiology 2016
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC6425468/
https://ncbi.nlm.nih.gov/pubmed/27450564
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/eurheartj/ehw307
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