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Novel desmoplakin mutations in familial Carvajal syndrome

Desmoplakin is encoded by DSP gene, whose altered function leads to skin and hair abnormalities, and heart diseases. The whole triad of these traits characterizes the Carvajal syndrome (CS). CS is an autosomal recessive genetic disorder, mapping on chromosome 6q24 and caused by mutations in DSP gene...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Acta Myol
Egile Nagusiak: YERMAKOVICH, DANAT, SIVITSKAYA, LARYSA, VAIKHANSKAYA, TATIYANA, DANILENKO, NINA, MOTUK, IRYNA
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Pacini Editore srl 2018
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC6416697/
https://ncbi.nlm.nih.gov/pubmed/30944905
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