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Structural investigation of Rett-inducing MeCP2 mutations()

X-ray structure of methyl-CpG binding domain (MBD) of MeCP2, an intrinsically disordered protein (IDP) involved in Rett syndrome, offers a rational basis for defining the spatial distribution for most of the sites where mutations responsible of Rett syndrome, RTT, occur. We have ascribed pathogenici...

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Detalhes bibliográficos
Publicado no:Genes Dis
Main Authors: Spiga, Ottavia, Gardini, Simone, Rossi, Nicole, Cicaloni, Vittoria, Pettini, Francesco, Niccolai, Neri, Santucci, Annalisa
Formato: Artigo
Idioma:Inglês
Publicado em: Chongqing Medical University 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6411616/
https://ncbi.nlm.nih.gov/pubmed/30906830
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.gendis.2018.09.005
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