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Alpha-1 Antitrypsin Substitution for Extrapulmonary Conditions in Alpha-1 Antitrypsin Deficient Patients

Alpha-1 antitrypsin deficiency (AATD) is a genetic disorder which most commonly manifests as pulmonary emphysema. Accordingly, alpha-1 antitrypsin (AAT) augmentation therapy aims to reduce the progression of emphysema, as achieved by life-long weekly slow-drip infusions of plasma-derived affinity-pu...

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Detalhes bibliográficos
Publicado no:Chronic Obstr Pulm Dis
Main Authors: Baranovski, Boris M., Schuster, Ronen, Nisim, Omer, Brami, Ido, Lior, Yotam, Lewis, Eli C.
Formato: Artigo
Idioma:Inglês
Publicado em: COPD Foundation Inc 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6361480/
https://ncbi.nlm.nih.gov/pubmed/30723784
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.15326/jcopdf.5.4.2017.0161
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