Two Cases of Progressive Familial Intrahepatic Cholestasis Type 2: Role of Surgery with Brief Review of Literature

Progressive familial intrahepatic cholestasis (PFIC) is a rare bile acid transporter defect and autosomal recessive disorder with type 2 being the most common type. Partial internal or external biliary diversion delays its progression to end-stage liver disease. Here, we discuss two cases of type 2...

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Bibliografske podrobnosti
izdano v:J Indian Assoc Pediatr Surg
Main Authors: Saha, Hinglaj, Tapanjyoti, Ghosh, Biswas, Somak, Mishra, Prafulla Kumar, Basu, Kalyani Saha, Chatterjee, Uttara
Format: Artigo
Jezik:Inglês
Izdano: Medknow Publications & Media Pvt Ltd 2019
Teme:
Case Report
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC6322173/
https://ncbi.nlm.nih.gov/pubmed/30686894
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/jiaps.JIAPS_235_17
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