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Iron metabolism under conditions of ineffective erythropoiesis in β-thalassemia

β-Thalassemia (BT) is an inherited genetic disorder that is characterized by ineffective erythropoiesis (IE), leading to anemia and abnormal iron metabolism. IE is an abnormal expansion of the number of erythroid progenitor cells with unproductive synthesis of enucleated erythrocytes, leading to ane...

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Dettagli Bibliografici
Pubblicato in:Blood
Autore principale: Rivella, Stefano
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society of Hematology 2019
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6318430/
https://ncbi.nlm.nih.gov/pubmed/30401707
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1182/blood-2018-07-815928
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