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Toll-like receptor 9 activation potentiates interferon-γ-mediated immunopathology in a murine model of Macrophage Activation Syndrome

OBJECTIVE: Macrophage Activation Syndrome (MAS) is a life-threatening cytokine storm syndrome that occurs in patients with underlying rheumatologic diseases. Preclinical and clinical data suggest that interferon (IFN)γ is pathogenic in MAS, yet how IFNγ causes disease remains unknown. In this manusc...

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Detalhes bibliográficos
Publicado no:Arthritis Rheumatol
Main Authors: Weaver, Lehn K., Niansheng, Chu, Behrens, Edward M.
Formato: Artigo
Idioma:Inglês
Publicado em: 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6310087/
https://ncbi.nlm.nih.gov/pubmed/30073799
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/art.40683
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