Caricamento...

PTBP1 acts as a dominant repressor of the aberrant tissue‐specific splicing of ISCU in hereditary myopathy with lactic acidosis

BACKGROUND: Hereditary myopathy with lactic acidosis (HML) is an autosomal recessive disease caused by an intron mutation in the iron‐sulfur cluster assembly (ISCU) gene. The mutation results in aberrant splicing, where part of the intron is retained in the final mRNA transcript, giving rise to a tr...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Pubblicato in:Mol Genet Genomic Med
Autori principali: Rawcliffe, Denise F. R., Österman, Lennart, Nordin, Angelica, Holmberg, Monica
Natura: Artigo
Lingua:Inglês
Pubblicazione: John Wiley and Sons Inc. 2018
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6305642/
https://ncbi.nlm.nih.gov/pubmed/30209894
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/mgg3.413
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !