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Transcriptional Regulation of the Huntingtin Gene

Huntington’s disease (HD) is an autosomal dominant neurodegenerative disorder caused by a CAG trinucleotide expansion in the HTT gene, which encodes for an abnormal polyglutamine tract in the huntingtin protein (HTT). This review examines the known mechanisms of HTT gene regulation. We discuss HTT e...

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Dettagli Bibliografici
Pubblicato in:J Huntingtons Dis
Autori principali: Thomson, Sarah B., Leavitt, Blair R.
Natura: Artigo
Lingua:Inglês
Pubblicazione: IOS Press 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6294578/
https://ncbi.nlm.nih.gov/pubmed/30452421
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3233/JHD-180331
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