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Blessing in disguise; a case of Hereditary Persistence of Fetal Hemoglobin

Fetal Hemoglobin (HbF, α2γ2) is produced from the eighth week of gestation, constitutes 60 – 80 % of total hemoglobin by birth, which is then replaced with adult Hemoglobin A1 (HbA1: α2β2) by 6–12 months. Hereditary Persistence of Fetal Hemoglobin (HPFH) is a rare benign asymptomatic genetic disorde...

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Pubblicato in:J Community Hosp Intern Med Perspect
Autori principali: Shaukat, Irfan, Pudal, Amrit, Yassin, Sayf, Höti, Naseruddin, Mustafa, Sadaf
Natura: Artigo
Lingua:Inglês
Pubblicazione: Taylor & Francis 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6292363/
https://ncbi.nlm.nih.gov/pubmed/30559951
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1080/20009666.2018.1536241
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