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Therapeutic potential of alpha-1 antitrypsin in human disease

Alpha-1 antitrypsin (AAT), an alpha globulin glycoprotein, is a member of the serine protease inhibitor (serpin) superfamily. The clinical significance of AAT is highlighted by AAT deficiency. Genetic deficiency of AAT can present as several neutrophilic diseases associated with emphysema, liver cir...

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Pubblicato in:Ann Pediatr Endocrinol Metab
Autori principali: Kim, Minsun, Cai, Qing, Oh, Youngman
Natura: Artigo
Lingua:Inglês
Pubblicazione: Korean Society of Pediatric Endocrinology 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6177666/
https://ncbi.nlm.nih.gov/pubmed/30286568
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.6065/apem.2018.23.3.131
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