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Human Dystrophin Structural Changes upon Binding to Anionic Membrane Lipids

Scaffolding proteins play important roles in supporting the plasma membrane (sarcolemma) of muscle cells. Among them, dystrophin strengthens the sarcolemma through protein-lipid interactions, and its absence due to gene mutations leads to the severe Duchenne muscular dystrophy. Most of the dystrophi...

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Publicado en:Biophys J
Autores principales: Dos Santos Morais, Raphael, Delalande, Olivier, Pérez, Javier, Mias-Lucquin, Dominique, Lagarrigue, Mélanie, Martel, Anne, Molza, Anne-Elisabeth, Chéron, Angélique, Raguénès-Nicol, Céline, Chenuel, Thomas, Bondon, Arnaud, Appavou, Marie-Sousai, Le Rumeur, Elisabeth, Combet, Sophie, Hubert, Jean-François
Formato: Artigo
Lenguaje:Inglês
Publicado: The Biophysical Society 2018
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6170597/
https://ncbi.nlm.nih.gov/pubmed/30197181
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bpj.2018.07.039
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