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Supplementation with a selective amino acid formula ameliorates muscular dystrophy in mdx mice

Duchenne muscular dystrophy (DMD) is one of the most common and severe forms of muscular dystrophy. Oxidative myofibre content, muscle vasculature architecture and exercise tolerance are impaired in DMD. Several studies have demonstrated that nutrient supplements ameliorate dystrophic features, ther...

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Bibliografske podrobnosti
izdano v:Sci Rep
Main Authors: Banfi, Stefania, D’Antona, Giuseppe, Ruocco, Chiara, Meregalli, Mirella, Belicchi, Marzia, Bella, Pamela, Erratico, Silvia, Donato, Elisa, Rossi, Fabio, Bifari, Francesco, Lonati, Caterina, Campaner, Stefano, Nisoli, Enzo, Torrente, Yvan
Format: Artigo
Jezik:Inglês
Izdano: Nature Publishing Group UK 2018
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC6168581/
https://ncbi.nlm.nih.gov/pubmed/30279586
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41598-018-32613-w
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