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A Regulatory Circuitry Between Gria2, miR-409, and miR-495 Is Affected by ALS FUS Mutation in ESC-Derived Motor Neurons

Mutations in fused in sarcoma (FUS) cause amyotrophic lateral sclerosis (ALS). FUS is a multifunctional protein involved in the biogenesis and activity of several types of RNAs, and its role in the pathogenesis of ALS may involve both direct effects of disease-associated mutations through gain- and...

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Dettagli Bibliografici
Pubblicato in:Mol Neurobiol
Autori principali: Capauto, Davide, Colantoni, Alessio, Lu, Lei, Santini, Tiziana, Peruzzi, Giovanna, Biscarini, Silvia, Morlando, Mariangela, Shneider, Neil A., Caffarelli, Elisa, Laneve, Pietro, Bozzoni, Irene
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer US 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6132778/
https://ncbi.nlm.nih.gov/pubmed/29430619
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s12035-018-0884-4
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