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A Transient Developmental Window of Fast-Spiking Interneuron Dysfunction in a Mouse Model of Dravet Syndrome

Dravet syndrome is a severe, childhood-onset epilepsy largely due to heterozygous loss-of-function mutation of the gene SCN1A, which encodes the type 1 neuronal voltage-gated sodium (Na(+)) channel α subunit Nav1.1. Prior studies in mouse models of Dravet syndrome (Scn1a(+/−) mice) indicate that, in...

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Pubblicato in:J Neurosci
Autori principali: Favero, Morgana, Sotuyo, Nathaniel P., Lopez, Emily, Kearney, Jennifer A., Goldberg, Ethan M.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Society for Neuroscience 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6125809/
https://ncbi.nlm.nih.gov/pubmed/30104343
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.0193-18.2018
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