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Molecular basis for defective glycosylation and Pseudomonas pathogenesis in cystic fibrosis lung

The CFTR gene encodes a transmembrane conductance regulator, which is dysfunctional in patients with cystic fibrosis (CF). The mechanism by which defective CFTR (CF transmembrane conductance regulator) leads to undersialylation of plasma membrane glycoconjugates, which in turn promote lung pathology...

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Hlavní autoři: Poschet, J. F., Boucher, J. C., Tatterson, L., Skidmore, J., Van Dyke, R. W., Deretic, V.
Médium: Artigo
Jazyk:Inglês
Vydáno: The National Academy of Sciences 2001
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC61151/
https://ncbi.nlm.nih.gov/pubmed/11717455
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.241182598
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