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Characterization of mutations in PRNP (prion) gene and their possible roles in neurodegenerative diseases

Abnormal prion proteins are responsible for several fatal neurodegenerative diseases in humans and in animals, including Creutzfeldt–Jakob disease (CJD), Gerstmann–Sträussler–Scheinker disease, and fatal familial insomnia. Genetics is important in prion diseases, but in the most cases, cause of dise...

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Detalhes bibliográficos
Publicado no:Neuropsychiatr Dis Treat
Main Authors: Bagyinszky, Eva, Giau, Vo Van, Youn, Young Chul, An, Seong Soo A, Kim, SangYun
Formato: Artigo
Idioma:Inglês
Publicado em: Dove Medical Press 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6097508/
https://ncbi.nlm.nih.gov/pubmed/30147320
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2147/NDT.S165445
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