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Bilateral Pheochromocytomas in a Patient with Y175C Von Hippel-Lindau Mutation

Von Hippel-Lindau (VHL) disease, caused by germline mutations in the VHL gene, is characterized by metachronously occurring tumors including pheochromocytoma, renal cell carcinoma (RCC), and hemangioblastoma. Although VHL disease leads to reduced life expectancy, its diagnosis is often missed and tu...

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Dades bibliogràfiques
Publicat a:Case Rep Endocrinol
Autors principals: Astapova, Olga, Biswas, Anindita, DiMauro, Alessandra, Moalem, Jacob, Hammes, Stephen R.
Format: Artigo
Idioma:Inglês
Publicat: Hindawi 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6076969/
https://ncbi.nlm.nih.gov/pubmed/30105105
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2018/8967159
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