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TNFa knockdown in the retina promotes cone survival in a mouse model of autosomal dominant retinitis pigmentosa

Expression of T17M rhodopsin (T17M) in rods activates the Unfolded Protein Response (UPR) and leads to the development of autosomal dominant retinitis pigmentosa (adRP). The rod death occurs in adRP retinas prior to cone photoreceptor death, so the mechanism by which cone photoreceptors die remains...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Biochim Biophys Acta
Egile Nagusiak: Rana, Tapasi, Kotla, Pravallika, Fullard, Roderick, Gorbatyuk, Marina
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2016
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC6056179/
https://ncbi.nlm.nih.gov/pubmed/27750040
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bbadis.2016.10.008
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