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Port-wine stain as a clue for two rare coexisting entities

Phakomatosis pigmentovascularis (PPV) is an uncommon dermatosis characterised by the presence of both pigmentary and vascular abnormalities.(1) Its pathogenesis is not elucidated, and the prognosis is mainly determined by the presence of extracutaneous manifestations, such as Klippel-Trenaunay syndr...

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Detalles Bibliográficos
Publicado en:BMJ Case Rep
Autores principales: Almeida, Filipa Tavares, Caldas, Regina, Duarte, Maria da Luz, Brito, Celeste
Formato: Artigo
Lenguaje:Inglês
Publicado: BMJ Publishing Group 2018
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6047724/
https://ncbi.nlm.nih.gov/pubmed/30007908
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2018-225721
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