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Port-wine stain as a clue for two rare coexisting entities

Phakomatosis pigmentovascularis (PPV) is an uncommon dermatosis characterised by the presence of both pigmentary and vascular abnormalities.(1) Its pathogenesis is not elucidated, and the prognosis is mainly determined by the presence of extracutaneous manifestations, such as Klippel-Trenaunay syndr...

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Dades bibliogràfiques
Publicat a:BMJ Case Rep
Autors principals: Almeida, Filipa Tavares, Caldas, Regina, Duarte, Maria da Luz, Brito, Celeste
Format: Artigo
Idioma:Inglês
Publicat: BMJ Publishing Group 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6047724/
https://ncbi.nlm.nih.gov/pubmed/30007908
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2018-225721
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