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Arterial fragility in kyphoscoliotic Ehlers-Danlos syndrome

Pathogenic variants in the lysyl-hydroxylase-1 gene (PLOD1) are responsible for the kyphoscoliotic type of Ehlers-Danlos syndrome (EDS). The disease is classically responsible for severe hypotonia at birth, progressive kyphoscoliosis, generalised joint hypermobility and scleral fragility. Arterial f...

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Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Cyhoeddwyd yn:BMJ Case Rep
Prif Awduron: Henneton, Pierrick, Legrand, Anne, Giunta, Cecilia, Frank, Michael
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: BMJ Publishing Group 2018
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC6040561/
https://ncbi.nlm.nih.gov/pubmed/29982180
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2018-224423
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