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Ciliated conical epithelial cell protrusions point towards a diagnosis of primary ciliary dyskinesia

BACKGROUND: Primary ciliary dyskinesia can result from a number of different ciliary defects that adversely affect ciliary function resulting markedly reduced or absent mucociliary clearance. Improvement in diagnostic testing is an area of current research. During diagnostic evaluation of PCD we obs...

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Dades bibliogràfiques
Publicat a:Respir Res
Autors principals: O’Callaghan, Chris, Rutman, Andrew, Williams, Gwyneth, Kulkarni, Neeta, Hayes, Joseph, Hirst, Robert A.
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6019300/
https://ncbi.nlm.nih.gov/pubmed/29940967
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12931-018-0782-3
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