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Pheochromocytoma and Paraganglioma in Neurofibromatosis type 1: frequent surgeries and cardiovascular crises indicate the need for screening

BACKGROUND: Pheochromocytomas and Paragangliomas (PCC/PGL) are rare endocrine tumors that are mostly benign, but often hormone producing, causing significant morbidity and mortality due to excess catecholamine secretion and cardiovascular crises. It is estimated that 30% of PCC/PGL are due to germli...

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Библиографические подробности
Опубликовано в: :Clin Diabetes Endocrinol
Главные авторы: Petr, Elisabeth Joye, Else, Tobias
Формат: Artigo
Язык:Inglês
Опубликовано: BioMed Central 2018
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC6013983/
https://ncbi.nlm.nih.gov/pubmed/29977594
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s40842-018-0065-4
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