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The fibrogenic chemokine CCL18 is associated with disease severity in Erdheim-Chester disease

Erdheim-Chester disease (ECD) is a rare histiocytosis, characterized by xanthogranulomatous tissue infiltration by foamy histiocytes. Fibrosis, a histologic hallmark of ECD, is responsible for lesion growth and clinical manifestations. Unraveling molecular fibrotic pathway in ECD would allow the ide...

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Publicat a:Oncoimmunology
Autors principals: Pacini, Greta, Cavalli, Giulio, Tomelleri, Alessandro, De Luca, Giacomo, Pacini, Guido, Ferrarini, Marina, Doglioni, Claudio, Dagna, Lorenzo
Format: Artigo
Idioma:Inglês
Publicat: Taylor & Francis 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5993512/
https://ncbi.nlm.nih.gov/pubmed/29900045
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1080/2162402X.2018.1440929
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